Klippel-Trenaunay Syndrome – An interesting syndrome in a Nigerian child

Authors

  • Abiola Omobonike Omobola Adekoya Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.
  • Adesola Olubunmi Adekoya Babcock University Teaching hospital, Ilisan-Remo, Ogun State
  • Solomon Olubodunrin riyibi Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.
  • Austin Chimuanya Egwuogu Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.
  • Ayopo Lucia Ajayi Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.
  • Ayodeji Anike Olatunji Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.

Keywords:

Capillary malformations, Congenital disorder, Klippel-Trenaunay syndrome, Limb hypertrophy, Varicosities

Abstract

Klippel-Trenaunay Syndrome (KTS) is a complex and unusual congenital angio-osteo-hypertrophic disorder where affected individuals have cutaneous hemangioma, venous and lymphatic malformations, and hemihypertrophy of the soft tissue and bones of the limb, causing limb asymmetry. We report a 4-year-old child with ipsilateral hemihypertrophy and cutaneous hemangioma, where KTS diagnosis was made despite being challenging.

Author Biographies

Abiola Omobonike Omobola Adekoya, Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.

Department of Radiology, Olabisi Onabanjo University Teaching Hospital, Sagamu, Nigeria.

Adesola Olubunmi Adekoya, Babcock University Teaching hospital, Ilisan-Remo, Ogun State

Department of Pediatrics, Babcock University Teaching Hospital, Ilisan, Nigeria.

 

Solomon Olubodunrin riyibi, Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.

Department of Pediatrics, Olabisi Onabanjo University Teaching Hospital, Sagamu, Nigeria

Austin Chimuanya Egwuogu, Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.

Department of Radiology, Olabisi Onabanjo University Teaching Hospital, Sagamu, Nigeria

Ayopo Lucia Ajayi, Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.

Department of Pediatrics, Olabisi Onabanjo University Teaching Hospital, Sagamu, Nigeria

Ayodeji Anike Olatunji, Olabisi Onabanjo University Teaching Hospital, Sagamu. Ogun State.

Department of Radiology, Olabisi Onabanjo University Teaching Hospital, Sagamu, Nigeria.

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Published

2025-05-01

How to Cite

1.
Adekoya AOO, Adekoya AO, riyibi SO, Egwuogu AC, Ajayi AL, Olatunji AA. Klippel-Trenaunay Syndrome – An interesting syndrome in a Nigerian child. Ethiop J Pediatr Child Health [Internet]. 2025 May 1 [cited 2025 May 17];20(1). Available from: https://ejpch.net/index.php/ejpch/article/view/202