Scimitar syndrome: A rare cause of respiratory distress in infants – Case report

Abstract

Scimitar syndrome is a rare combination of congenital cardiopulmonary anomalies that includes a partially anomalous right pulmonary vein (PARPV) from the right lung. Here we report an infant who presented with recurrent respiratory tract infections, respiratory distress and persistent pulmonary hypertension who was diagnosed to have scimitar syndrome. The diversity of the clinical presentation and its rarity itself make it difficult to diagnose. Here we intend to highlight the importance of key diagnostic investigations such as chest X-rays, echocardiograms and computerized tomography in arriving at the diagnosis. A high degree of suspicion is required to arrange crucial investigations without delay.